Abstract : <p>Dental anomalies are the formative defects that occur as a result of multifactorial interactions between genetic or environmental factors during the process of tooth development. Literature has revealed presence of multiple dental anomalies such as supernumerary tooth, tooth agenesis, ectopic tooth eruption, atypical tooth size or shape, taurodontism, pulp stones etc in various syndromic or non-syndromic conditions. Although asymptomatic, but early diagnosis is requisite for better patient management to prevent the occurrence of associated complications. Here, we report a rare case of 23-year-old male patient who presented with cardiovascular manifestations along with multiple dental and skeletal findings. Such combination of dental and skeletal findings has not been reported earlier in association with any individual syndrome. Hence, we propose it to be a new syndrome of non-genetic type associated with multiple cardiac, skeletal and dental anomalies.</p>