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Vol - 28, Issue - 05
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[This article belongs to Volume - 28, Issue - 05]
International Medical Journal
Journal ID
:
IMJ-07-08-2021-837
Total View
:
738
Title
:
Spontaneous upper and lower extremity Ecchymosis: Unusual Presentation of Systemic Amyloidosis
Abstract
: <p>Amyloidosis is a group of heterogeneous diseases characterized by extracellular deposition of proteinaceous material in various organs. Multiple dermatological manifestations of amyloidosis have been described, including nodules, papules, plaques and periorbital ecchymosis. We report a case of idiopathic primary systemic amyloidosis presenting with unusual extensive upper and lower limbs ecchymoses along with laryngeocel, lacking the classical presentation of macroglossia, waxy papules, and plaques.</p>
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